PFAM ID:GO:0043233
Term :organelle lumen
Entrez Gene IDs are linked to their corresponding NCBI GenBank entry.
Gene symbols are linked to the entry for the gene in the HD Research CrossRoads database.
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Entrez Gene IDApproved SymbolApproved Name
34ACADMacyl-CoA dehydrogenase_ C-4 to C-12 straight chain
38ACAT1acetyl-CoA acetyltransferase 1
60ACTBactin_ beta
87ACTN1actinin_ alpha 1
88ACTN2actinin_ alpha 2
207AKT1v-akt murine thymoma viral oncogene homolog 1
467ATF3activating transcription factor 3
498ATP5A1ATP synthase_ H+ transporting_ mitochondrial F1 complex_ alpha subunit 1_ cardiac muscle
506ATP5BATP synthase_ H+ transporting_ mitochondrial F1 complex_ beta polypeptide
513ATP5DATP synthase_ H+ transporting_ mitochondrial F1 complex_ delta subunit
515ATP5F1ATP synthase_ H+ transporting_ mitochondrial Fo complex_ subunit B1
836CASP3caspase 3_ apoptosis-related cysteine peptidase
875CBScystathionine-beta-synthase
891CCNB1cyclin B1
988CDC5LCDC5 cell division cycle 5-like (S. pombe)
1072CFL1cofilin 1 (non-muscle)
1073CFL2cofilin 2 (muscle)
1385CREB1cAMP responsive element binding protein 1
1387CREBBPCREB binding protein
1431CScitrate synthase
1457CSNK2A1casein kinase 2_ alpha 1 polypeptide
1499CTNNB1catenin (cadherin-associated protein)_ beta 1_ 88kDa
1737DLATdihydrolipoamide S-acetyltransferase
1743DLSTdihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex)
1849DUSP7dual specificity phosphatase 7
1950EGFepidermal growth factor
2071ERCC3excision repair cross-complementing rodent repair deficiency_ complementation group 3 (xeroderma pigmentosum group B complementing)
2073ERCC5excision repair cross-complementing rodent repair deficiency_ complementation group 5
2243FGAfibrinogen alpha chain
2521FUSFused in sarcoma
2547XRCC6X-ray repair complementing defective repair in Chinese hamster cells 6
2648KAT2AK(lysine) acetyltransferase 2A
3065HDAC1histone deacetylase 1
3066HDAC2histone deacetylase 2
3091HIF1Ahypoxia inducible factor 1_ alpha subunit (basic helix-loop-helix transcription factor)
3146HMGB1high-mobility group box 1
3148HMGB2high-mobility group box 2
3162HMOX1heme oxygenase (decycling) 1
3178HNRNPA1heterogeneous nuclear ribonucleoprotein A1
3297HSF1heat shock transcription factor 1
3309HSPA5heat shock 70kDa protein 5 (glucose-regulated protein_ 78kDa)
3313HSPA9heat shock 70kDa protein 9 (mortalin)
3337DNAJB1DnaJ (Hsp40) homolog_ subfamily B_ member 1
3479IGF1insulin-like growth factor 1 (somatomedin C)
3646EIF3Eeukaryotic translation initiation factor 3_ subunit E
3710ITPR3inositol 1_4_5-triphosphate receptor_ type 3
3725JUNjun proto-oncogene
3843IPO5importin 5
4255MGMTO-6-methylguanine-DNA methyltransferase
4790NFKB1nuclear factor of kappa light polypeptide gene enhancer in B-cells 1
4803NGFnerve growth factor (beta polypeptide)
4809NHP2L1NHP2 non-histone chromosome protein 2-like 1 (S. cerevisiae)
4928NUP98nucleoporin 98kDa
4967OGDHoxoglutarate (alpha-ketoglutarate) dehydrogenase (lipoamide)
4968OGG18-oxoguanine DNA glycosylase
5160PDHA1pyruvate dehydrogenase (lipoamide) alpha 1
5347PLK1polo-like kinase 1
5356PLRG1pleiotropic regulator 1 (PRL1 homolog_ Arabidopsis)
5430POLR2Apolymerase (RNA) II (DNA directed) polypeptide A_ 220kDa
5431POLR2BPolymerase (RNA) II (DNA directed) polypeptide B_ 140kDa
5499PPP1CAprotein phosphatase 1_ catalytic subunit_ alpha isozyme
5557PRIM1primase_ DNA_ polypeptide 1 (49kDa)
5594MAPK1mitogen-activated protein kinase 1
5595MAPK3mitogen-activated protein kinase 3
5705PSMC5proteasome (prosome_ macropain) 26S subunit_ ATPase_ 5
5714PSMD8proteasome (prosome_ macropain) 26S subunit_ non-ATPase_ 8
5743PTGS2prostaglandin-endoperoxide synthase 2 (prostaglandin G/H synthase and cyclooxygenase)
5901RANRAN_ member RAS oncogene family
6125RPL5ribosomal protein L5
6187RPS2ribosomal protein S2
6189RPS3Aribosomal protein S3A
6199RPS6KB2ribosomal protein S6 kinase_ 70kDa_ polypeptide 2
6209RPS15Ribosomal protein S15
6500SKP1S-phase kinase-associated protein 1
6601SMARCC2SWI/SNF related_ matrix associated_ actin dependent regulator of chromatin_ subfamily c_ member 2
6628SNRPBsmall nuclear ribonucleoprotein polypeptides B and B1
6632SNRPD1small nuclear ribonucleoprotein D1 polypeptide 16kDa
6633SNRPD2small nuclear ribonucleoprotein D2 polypeptide 16.5kDa
6634SNRPD3small nuclear ribonucleoprotein D3 polypeptide 18kDa
6636SNRPFsmall nuclear ribonucleoprotein polypeptide F
6637SNRPGsmall nuclear ribonucleoprotein polypeptide G
6647SOD1superoxide dismutase 1_ soluble
6667SP1Sp1 transcription factor
6749SSRP1structure specific recognition protein 1
6829SUPT5Hsuppressor of Ty 5 homolog (S. cerevisiae)
6874TAF4TAF4 RNA polymerase II_ TATA box binding protein (TBP)-associated factor_ 135kDa
6875TAF4BTAF4b RNA polymerase II_ TATA box binding protein (TBP)-associated factor_ 105kDa
7029TFDP2transcription factor Dp-2 (E2F dimerization partner 2)
7157TP53tumor protein p53
7251TSG101tumor susceptibility gene 101
7307U2AF1U2 small nuclear RNA auxiliary factor 1
7314UBBubiquitin B
7329UBE2Iubiquitin-conjugating enzyme E2I (UBC9 homolog_ yeast)
7341SUMO1SMT3 suppressor of mif two 3 homolog 1 (S. cerevisiae)
7345UCHL1Ubiquitin carboxyl-terminal esterase L1 (ubiquitin thiolesterase)
7415VCPvalosin-containing protein
7417VDAC2voltage-dependent anion channel 2
7422VEGFAvascular endothelial growth factor A
7456WIPF1WAS/WASL interacting protein family_ member 1
7469WHSC2Wolf-Hirschhorn syndrome candidate 2
7936RDBPRD RNA binding protein
7942TFEBtranscription factor EB
8295TRRAPtransformation/transcription domain-associated protein
8454CUL1cullin 1
8568RRP1ribosomal RNA processing 1 homolog (S. cerevisiae)
8721EDF1endothelial differentiation-related factor 1
8841HDAC3histone deacetylase 3
9126SMC3Structural maintenance of chromosomes 3
9184BUB3budding uninhibited by benzimidazoles 3 homolog (yeast)
9252RPS6KA5ribosomal protein S6 kinase_ 90kDa_ polypeptide 5
9439MED23mediator complex subunit 23
9734HDAC9histone deacetylase 9
9759HDAC4histone deacetylase 4
9869SETDB1SET domain_ bifurcated 1
9972NUP153nucleoporin 153kDa
10013HDAC6histone deacetylase 6
10014HDAC5histone deacetylase 5
10105PPIFpeptidylprolyl isomerase F
10171RCL1RNA terminal phosphate cyclase-like 1
10569SLU7SLU7 splicing factor homolog (S. cerevisiae)
10576CCT2chaperonin containing TCP1_ subunit 2 (beta)
10594PRPF8PRP8 pre-mRNA processing factor 8 homolog (S. cerevisiae)
10891PPARGC1Aperoxisome proliferator-activated receptor gamma_ coactivator 1 alpha
10946SF3A3splicing factor 3a_ subunit 3_ 60kDa
11198SUPT16Hsuppressor of Ty 16 homolog (S. cerevisiae)
11224RPL35ribosomal protein L35
22938SNW1SNW domain containing 1
22948CCT5chaperonin containing TCP1_ subunit 5 (epsilon)
22985ACIN1apoptotic chromatin condensation inducer 1
23160WDR43WD repeat domain 43
23212RRS1RRS1 ribosome biogenesis regulator homolog (S. cerevisiae)
23410SIRT3sirtuin 3
23411SIRT1sirtuin 1
23451SF3B1splicing factor 3b_ subunit 1_ 155kDa
23481PES1pescadillo homolog 1_ containing BRCT domain (zebrafish)
23517SKIV2L2Superkiller viralicidic activity 2-like 2 (S. cerevisiae)
23560GTPBP4GTP binding protein 4
23636NUP62nucleoporin 62kDa
25896INTS7integrator complex subunit 7
25920COBRA1cofactor of BRCA1
25926NOL11nucleolar protein 11
25942SIN3ASIN3 homolog A_ transcription regulator (yeast)
26121PRPF31PRP31 pre-mRNA processing factor 31 homolog (S. cerevisiae)
27339PRPF19PRP19/PSO4 pre-mRNA processing factor 19 homolog (S. cerevisiae)
51176LEF1lymphoid enhancer-binding factor 1
51340CRNKL1crooked neck pre-mRNA splicing factor-like 1 (Drosophila)
51343FZR1fizzy/cell division cycle 20 related 1 (Drosophila)
51497TH1LTH1-like (Drosophila)
51616TAF9BTAF9B RNA polymerase II_ TATA box binding protein (TBP)-associated factor_ 31kDa
51692CPSF3cleavage and polyadenylation specific factor 3_ 73kDa
51701NLKnemo-like kinase
54623PAF1Paf1_ RNA polymerase II associated factor_ homolog (S. cerevisiae)
55299BXDC2Brix domain-containing protein 2
55656INTS8integrator complex subunit 8
55756INTS9integrator complex subunit 9
55869HDAC8histone deacetylase 8
56949XAB2XPA binding protein 2
57461ISY1ISY1 splicing factor homolog (S. cerevisiae)
57508INTS2integrator complex subunit 2
64714PDIA2protein disulfide isomerase family A_ member 2
79885HDAC11histone deacetylase 11
80789INTS5integrator complex subunit 5
83933HDAC10histone deacetylase 10
84313VPS25vacuolar protein sorting 25 homolog (S. cerevisiae)
84447SYVN1synovial apoptosis inhibitor 1_ synoviolin
84823LMNB2lamin B2
92105INTS4integrator complex subunit 4
266743NPAS4neuronal PAS domain protein 4